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Sep. 10, 2014:
A total of 174 experimentally verified S-nitrosylation sites on 94 S-nitrosylated proteins from individualized human colorectal cancer tissues using a label-free quantitation strategy.

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Protein Name: Alpha-aminoadipic semialdehyde dehydrogenase

UniprotKB/SwissProt ID: AL7A1_HUMAN (P49419)

Gene Name: ALDH7A1

Synonyms: ATQ1

Organism: Homo sapiens (Human).

Function: Multifunctional enzyme mediating important protective effects. Metabolizes betaine aldehyde to betaine, an important cellular osmolyte and methyl donor. Protects cells from oxidative stress by metabolizing a number of lipid peroxidation-derived aldehydes. Involved in lysine catabolism.

Other Modifications: View all modification sites in dbPTM

Protein Subcellular Localization: Mitochondrion. Nucleus. Isoform 2: Cytoplasm, cytosol.

PDB :
( If your security settings prevent Jmol from running, please register http://140.138.144.145/ as a safe location in your Java settings. )

Protein disease:
Disease database Database Entry Disease information
HPRD00124Epilepsy, pyridoxine-dependent
Network with metabolic pathway:
Kegg map ID Pathway Link
map00010Glycolysis / Gluconeogenesis
map00053Ascorbate and aldarate metabolism
map00071Fatty acid metabolism
map00260"Glycine, serine and threonine metabolism"
map00280"Valine, leucine and isoleucine degradation"
map00310Lysine degradation
map00330Arginine and proline metabolism
map00340Histidine metabolism
map00380Tryptophan metabolism
map00410beta-Alanine metabolism
map00561Glycerolipid metabolism
map00620Pyruvate metabolism
map00640Propanoate metabolism
Graphical Visualization of S-nitrosylation Sites:
Overview of Protein S-nitrosylation Sites with Functional and Structural Information
InterPro ID Domain
IPR015590