Protein Name: Trifunctional enzyme subunit alpha, mitochondrial
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UniprotKB/SwissProt ID: ECHA_HUMAN (P40939)
Gene Name: HADHA
Synonyms: HADH
Organism: Homo sapiens (Human).
Function: Bifunctional subunit.
Other Modifications: View all modification sites in dbPTM
Protein Subcellular Localization: Mitochondrion.
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Protein disease:
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Disease database |
Database Entry |
Disease information | HPRD | 02934 | LChad deficiency | HPRD | 02934 | Neuropathy-myopathy, progressive, due to trifunctional protein deficiency | HPRD | 02934 | Trifunctional protein deficiency |
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Network with metabolic pathway:
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Graphical Visualization of S-nitrosylation Sites:
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Overview of Protein S-nitrosylation Sites with Functional and Structural Information | |
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