Protein Name: 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
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UniprotKB/SwissProt ID: ODBA_MOUSE (P50136)
Gene Name: Bckdha
Organism: Mus musculus (Mouse).
Function: The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3).
Other Modifications: View all modification sites in dbPTM
Protein Subcellular Localization: Mitochondrion matrix.
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Graphical Visualization of S-nitrosylation Sites:
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Overview of Protein S-nitrosylation Sites with Functional and Structural Information | |
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